A Case of Paraneoplastic Elastosis Perforans Serpiginosa Associated with T-Cell Non-Hodgkin Lymphoma

Abstract

Perforating dermatoses are a group of diseases characterized by
transepidermal elimination of dermal material. This
group is
divided into four subgroups: Kyrle disease, reactive perforating
collagenosis, elastosis perforans
serpiginosa and
perforating
folliculitis. They can be primary or secondary. Secondary
perforating dermatoses may develop due to chronic renal failu
re,
diabetes mellitus, autoimmune diseases and malignancies. With
elastosis perforans serpiginosa, the rarest of this group,
transepidermal elimination of dermal elastin tissue is present. It
may be idiopathic but may also
develop Down
syndrome, Ehlers
-
Da
nlos syndrome, Marfan's syndrome, osteogenesis imperfecta,
acrogeria, Rothound
-
Thomson syndrome, cutislaxa and due to
using D
-
penicillamine medication. Here in is presented, as the
second case in the literature, a 60
-
year
-
old patient with
paraneoplastic EP
S associated with T
-
cell non
-
Hodgkin lymphoma