Ectrodactyly –Rare Indian Disorder : A Case Report

Abstract

Ectrodactyly or Split Hand & Split Foot Malformation (SHFM)
is congenital absence of one or more
central/median rays or digits creating cone shaped clef
ts of hands and/or feet.
(1)(2
)
Term ectrodactyly
was originated from greek words
-
Ektroma (abortion) and Daktylos (Finger).
Incidence reported is
1:90,000 live births
with no sex predilection
.
Ist documented case was in a tribe of Guiana Indians in
1770.
(
2
)
It was called “Crab claw” deformity for first time by Von Walker in 1829 and “Lobster claw” by
Cruveilhier in 1842.
(3
)
I
t is also known as K
arsc
h Neugebauer Syndrome